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Clinical management of CF » Nutritional support

Nutritional support

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The importance of maintaining good nutrition cannot be overstated and impacts long-term survival and lung health to a significant extent.16 Supplementation with fat-soluble vitamins and pancreatic enzymes is essential for individuals with pancreatic insufficiency.

Moreover, as up to 30% of adult patients have cystic fibrosis-related diabetes (CFRD),15 it is one of the most important co-morbidities of CF. Management of CFRD greatly differs from type 1 diabetes: most patients need treatment with insulin and little or no change in dietary habits.

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  11. Smyth, T et al. Arch Dis Child Educ Pract Ed 2005;90:1–6
  12. Report of the UK Cystic Fibrosis Trust Antibiotic Working Group 2009 ISBN 0-9548511-3-7
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  14. O’Sullivan B et al. Lancet 2009;373:1891–904
  15. Anon. Bethesda MD. Cystic Fibrosis Foundation Patient Registry 2007
  16. Ratjen FA. Respir Care 2009;54:595–605